Recombinant Human Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial (MCCC1) MBS1427768 from MyBioSource.com

Description

This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism

Product Specs
ItemRecombinant Human Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial (MCCC1)
CompanyMyBioSource.com
Price Pricing Info Supplier Page View Company Product Page
Catalog NumberMBS1427768
Quantity0.02 mg (E-Coli)
PurityGreater or equal to 85% purity as determined by SDS-PAGE
TypeRecombinant Protein
Molecule NameMethylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial (MCCC1)
Domain/Region/Terminus42-725, Full length protein
NCBI Full Gene Namemethylcrotonyl-CoA carboxylase subunit 1
NCBI Gene AliasesMCCA, MCC-B, MCCCalpha
FormatLyophilized or liquid (Format to be determined during the manufacturing process)
Molecular Weight80,473 Da
Source/Expression SystemE Coli or Yeast or Baculovirus or Mammalian Cell

Sequence

TTATGRNITK VLIANRGEIA CRVMRTAKKL GVQTVAVYSE ADRNSMHVDM ADEAYSIGPA PSQQSYLSME KIIQVAKTSA AQAIHPGCGF LSENMEFAEL CKQEGIIFIG PPPSAIRDMG IKSTSKSIMA AAGVPVVEGY HGEDQSDQCL KEHARRIGYP VMIKAVRGGG GKGMRIVRSE QEFQEQLESA RREAKKSFND DAMLIEKFVD TPRHVEVQVF GDHHGNAVYL FERDCSVQRR HQKIIEEAPA PGIKSEVRKK LGEAAVRAAK AVNYVGAGTV EFIMDSKHNF CFMEMNTRLQ VEHPVTEMIT GTDLVEWQLR IAAGEKIPLS QEEITLQGHA FEARIYAEDP SNNFMPVAGP LVHLSTPRAD PSTRIETGVR QGDEVSVHYD PMIAKLVVWA ADRQAALTKL RYSLRQYNIV GLHTNIDFLL NLSGHPEFEA GNVHTDFIPQ HHKQLLLSRK AAAKESLCQA ALGLILKEKA MTDTFTLQAH DQFSPFSSSS GRRLNISYTR NMTLKDGKNN VAIAVTYNHD GSYSMQIEDK TFQVLGNLYS EGDCTYLKCS VNGVASKAKL IILENTIYLF SKEGSIEIDI PVPKYLSSVS SQETQGGPLA PMTGTIEKVF VKAGDKVKAG DSLMVMIAMK MEHTIKSPKD GTVKKVFYRE GAQANRHTPL VEFEEEESDK RESE

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